Pulmonary hypertension (PH) is a pathophysiological status characterized by a mean pulmonary arterial pressure of at least 25 mmHg (1 mmHg=0.133 kPa) at rest measured by right heart catheterization. Chronic PH will increase the afterload of right ventricular and eventually lead to right heart failure. Hemodynamic changes in normal pregnancy can exacerbate the right ventricular burden in pregnant women with PH, sequentially causing right heart failure and following circulatory failure. The aim of this review is to summarize the perioperative management experience by reviewing the epidemiology and pathophysiology of PH, the influence of pregnancy on PH and anesthesia for delivery with PH, which provides a theoretical basis for clinical practice. It is currently considered, that pregnant women with PH should be treated with multidisciplinary team therapy before delivery. The cesarean section with spinal anesthesia in 34－36 weeks of pregnancy is recommended. Maternal ICU treatment is preferably provided after delivery. This review is intended to improve maternal and neonatal prognosis and reduce maternal mortality in pregnancy with PH by enhancing perioperative management.